Adamantinoma of long bones is a rare primary bone tumor. Approximately
100 cases have been reported in the literature. In the fourteen cases we
studied in detail the ages of the patients ranged from thirteen to
sixty-seven years and there were as many males as females. Twelve of the
lesions were located in the tibia and two, in the humerus. The
roentgenographic findings were sharply defined eccentric lobular lesions in
the diaphysis. Some of the lesions were lytic and coarsely trabecular with
a honeycomb appearance occasionally associated with periosteal new-bone
formation. A sawtooth area of cortical-bone loss was found to be
characteristic of this lesion. A microscopic finding is presented to
support the theory of angioblastic origin of this tumor. The most
successful treatment was amputation. Less often en bloc excision succeeded.
Metastases to other bones, regional lymph nodes, and the lung were
recorded.