Scoliosis was evident in eighteen of eighty-eight patients with
arthrogryposis multiplex congenita. The predominant pattern of spinal
deformity was a structural thoracolumbar double curve that extended to the
sacrum and was associated with pelvic obliquity and lumbar hyperlordosis.
Significant contractures about the hips, dislocation of the hip, or both
were present in all patients but one. Most of the curves were progressive
and they became rigid and fixed at an early age. There was progression of
the pelvic obliquity coincident with progression of the curve. Treatment by
corrective casts or a Milwaukee brace was ineffective and if surgical
treatment directed at the pelvic obliquity did not correct that deformity,
spine fusion to the sacrum appeared necessary.