We evaluated the cases of twenty-three patients with thirty-six
congenital proximal radio-ulnar synostoses who had been followed between
1938 and 1984. None of the patients had had any attempt at surgical
correction or any ipsilateral congenital anomalies. Emphasis was placed on
analyzing the natural history of the lesion in these patients who had not
been operated on, and on determining the effect of a fixed position of the
forearm on function. Ten patients had unilateral and thirteen, bilateral
synostosis. Their mean age when last examined was twenty-two years (range,
three to fifty years). Eight patients were female and fifteen, male. The
forearms were fixed in an average of 30 degrees of pronation. The position
of the forearm was not found to be related to subjective functional
limitations, employment status, or the results of the hand-function test of
Jebsen et al. Most patients had few or no functional limitations, and were
employed in jobs that demanded extensive use of the forearm. Contrary to
the findings of other studies, we observed four distinct radiographic
patterns based on the presence of an osseous synostosis and the position of
the radial head. However, we noted no relationship between any of these
patterns and function. We concluded that operative treatment of congenital
radio-ulnar synostosis is rarely indicated, that less emphasis should be
placed on the single factor of the position of the forearm, and that
objective functional tests should be included in the assessment of these
patients.