JBJS | Familial Osteofibrous Dysplasia: A Case Series

The Journal of Bone & Joint Surgery, Volume 87, Issue 10

Scientific Articles | October 01, 2005

Familial Osteofibrous Dysplasia: A Case Series

Lori A. Karol, MD¹; David S. Brown, MD²; Carol A. Wise, PhD¹; Michael Waldron, MD¹

¹ Departments of Orthopaedic Surgery (L.A.K.) and Pathology (M.W.) and the Sarah M. and Charles E. Seay Center for Musculoskeletal Research (C.A.W.), Texas Scottish Rite Hospital for Children, 2222 Welborn, Dallas, TX 75219. E-mail address for L.A. Karol: lori.karol@tsrh.org
² Department of Orthopaedics, Cook Children's Hospital, 801 Seventh Avenue, Fort Worth, TX 76104

The Journal of Bone & Joint Surgery. 2005; 87:2297-2307 doi:10.2106/JBJS.D.02575

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Extract

Osteofibrous dysplasia is a benign bone dysplasia in which lytic lesions occur in the cortex of the tibia and/or fibula in skeletally immature patients. Campanacci proposed the term "osteofibrous dysplasia" and described the clinical and pathologic findings1,2. The dysplasia may be clinically silent, so the true incidence of the disease is unknown. Symptomatic children present with anterolateral bowing of the affected bones or with pathologic fractures. As a result of the site of involvement and the propensity for pathologic fractures, this condition may be confused with congenital pseudarthrosis of the tibia.

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Topics

tibia ; osteofibrous dysplasia ; fracture ; fibula ; lytic lesion

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These activities have been planned and implemented in accordance with the Essential Areas and policies of the Accreditation Council for Continuing Medical Education (ACCME) through the joint sponsorship of the American Academy of Orthopaedic Surgeons and The Journal of Bone and Joint Surgery, Inc. The American Academy of Orthopaedic Surgeons is accredited by the ACCME to provide continuing medical education for physicians.

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